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Mouse Anti-MIPEP (AA 611-713) Recombinant Antibody (CBFYM-2236) (CBMAB-M2419-FY)

This product is mouse antibody that recognizes MIPEP. The antibody CBFYM-2236 can be used for immunoassay techniques such as: ELISA, WB.
See all MIPEP antibodies

Summary

Host Animal
Mouse
Specificity
Human
Clone
CBFYM-2236
Antibody Isotype
IgG2a, k
Application
ELISA, WB

Basic Information

Immunogen
Recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.Immunogen sequence: PYVPNTAWQL RFSHLVGYGA RYYSYLMSRA VASMVWKECF LQDPFNRAAG ERYRREMLAH GGGREPMLMV EGMLQKCPSV DDFVSALVSD LDLDFETFLM DSE
Specificity
Human
Antibody Isotype
IgG2a, k
Clonality
Monoclonal
Application Notes
The COA includes recommended starting dilutions, optimal dilutions should be determined by the end user.

Formulations & Storage [For reference only, actual COA shall prevail!]

Format
Liquid
Storage
Store at +4°C short term (1-2 weeks). Aliquot and store at -20°C long term. Avoid repeated freeze/thaw cycles.
Epitope
AA 611-713

Target

Full Name
mitochondrial intermediate peptidase
Introduction
The product of this gene performs the final step in processing a specific class of nuclear-encoded proteins targeted to the mitochondrial matrix or inner membrane. This protein is primarily involved in the maturation of oxidative phosphorylation -related proteins. This gene may contribute to the functional effects of frataxin deficiency and the clinical manifestations of Friedreich ataxia.
Entrez Gene ID
4285
UniProt ID
Q99797
Alternative Names
Mitochondrial Intermediate Peptidase; EC 3.4.24.59; MIP; COXPD31; HMIP
Function
Cleaves proteins, imported into the mitochondrion, to their mature size.
Biological Process
Peptide metabolic process Source: GO_Central
Protein processing involved in protein targeting to mitochondrion Source: GO_Central
Proteolysis Source: GO_Central
Cellular Location
Mitochondrion matrix
Involvement in disease
Combined oxidative phosphorylation deficiency 31 (COXPD31):
An autosomal recessive, severe mitochondrial disease with multisystemic manifestations appearing soon after birth or in early infancy. Clinical features include left ventricular non-compaction, global developmental delay, severe hypotonia, seizures, cataract, and abnormal movements. Death may occur in early childhood.
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For research use only. Not intended for any clinical use.

Custom Antibody Labeling

We also offer labeled antibodies developed using our catalog antibody products and nonfluorescent conjugates (HRP, AP, Biotin, etc.) or fluorescent conjugates (Alexa Fluor, FITC, TRITC, Rhodamine, Texas Red, R-PE, APC, Qdot Probes, Pacific Dyes, etc.).

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