Rabbit Anti-QRSL1 Recombinant Antibody (RB37609) (CBMAB-1880-YC)

Name: Rabbit Anti-QRSL1 Recombinant Antibody (RB37609)
SKU: CBMAB-1880-YC
Rating: 5 (1 reviews)

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Datasheet

SDS

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Basic Information

Host Animal

Rabbit

Clone

RB37609

Application

ELISA, WB

Immunogen

A KLH conjugated synthetic peptide between 129-156 amino acids from the N-terminal region of human QRSL1

Specificity

Human

Antibody Isotype

IgG

Clonality

Monoclonal

Application Notes

The COA includes recommended starting dilutions, optimal dilutions should be determined by the end user.

Formulations & Storage [For reference only, actual COA shall prevail!]

Storage

Store at 4°C short term (1-2 weeks). Aliquot and store at -20°C long term. Avoid repeated freeze/thaw cycles.

Epitope

Localized in a.a.129-156

More Infomation

Target

Full Name

Glutaminyl-TRNA Synthase (Glutamine-Hydrolyzing)-Like 1

Introduction

QRSL belongs to the amidase family. QRSL1 allows the formation of correctly charged Gln-tRNA(Gln) through the transamidation of misacylated Glu-tRNA(Gln) in the mitochondria.

Entrez Gene ID

55278

UniProt ID

Q9H0R6

Alternative Names

GatA

Function

Allows the formation of correctly charged Gln-tRNA(Gln) through the transamidation of misacylated Glu-tRNA(Gln) in the mitochondria. The reaction takes place in the presence of glutamine and ATP through an activated gamma-phospho-Glu-tRNA(Gln).

Biological Process

Biological Process glutaminyl-tRNAGln biosynthesis via transamidationManual Assertion Based On ExperimentIDA:UniProtKB
Biological Process mitochondrial translationManual Assertion Based On ExperimentIMP:UniProtKB
Biological Process regulation of protein stabilityIEA:Ensembl

Cellular Location

Mitochondrion

Involvement in disease

Combined oxidative phosphorylation deficiency 40 (COXPD40):
An autosomal recessive mitochondrial disorder characterized by prenatal or infantile onset, fetal hydrops, severe hypertrophic cardiomyopathy, poor growth, sensorineural hearing loss, hepatic dysfunction, lactic acidosis, and decreased activities of mitochondrial respiratory complexes I, III, IV, and V. The disorder is lethal, with death occurring in infancy.

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Please try the standard protocols which include: protocols, troubleshooting and guide.

Enzyme-linked Immunosorbent Assay (ELISA)
Flow Cytometry
Immunofluorescence (IF)
Immunohistochemistry (IHC)
Immunoprecipitation (IP)
Western Blot (WB)
Enzyme Linked Immunospot (ELISpot)
Proteogenomic
Other Protocols

Isotype control

For research use only. Not intended for any clinical use.

Custom Antibody Labeling

We also offer labeled antibodies developed using our catalog antibody products and nonfluorescent conjugates (HRP, AP, Biotin, etc.) or fluorescent conjugates (Alexa Fluor, FITC, TRITC, Rhodamine, Texas Red, R-PE, APC, Qdot Probes, Pacific Dyes, etc.).

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