ALDH6A1
ALDH6A1 is a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible o
Full Name
Aldehyde Dehydrogenase 6 Family Member A1
Function
Plays a role in valine and pyrimidine metabolism. Binds fatty acyl-CoA.
Biological Process
Branched-chain amino acid catabolic process Source: Reactome
Brown fat cell differentiation Source: Ensembl
Thymine catabolic process Source: BHF-UCL
Thymine metabolic process Source: UniProtKB
Valine catabolic process Source: BHF-UCL
Valine metabolic process Source: UniProtKB
Brown fat cell differentiation Source: Ensembl
Thymine catabolic process Source: BHF-UCL
Thymine metabolic process Source: UniProtKB
Valine catabolic process Source: BHF-UCL
Valine metabolic process Source: UniProtKB
Cellular Location
Mitochondrion
Involvement in disease
Methylmalonate semialdehyde dehydrogenase deficiency (MMSDHD): A metabolic disorder characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.
View more
Anti-ALDH6A1 antibodies
+ Filters
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1, κ
Specificity: Human, Mouse, Rat
Clone: C9
Application*: E, IC, IF, IH, WB
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: 6H9B7
Application*: WB, FC, E, IH, IF
Target: ALDH6A1
Sensitivity: 0.028 ng/mL
Detection Range: 0.05-15 ng/mL
Sample Type: Serum, Plasma, cell culture supernates
Specificity: Human
Assay Type: Sandwich
Reactivity: Human
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: CBT4230
Application*: WB, IH, IC, F
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: CBT3858
Application*: IH, IC, F
More Infomation
Hot products 
-
Mouse Anti-GDF5 Recombinant Antibody (1F4) (CBMAB-G2740-LY)
-
Mouse Anti-DDC Recombinant Antibody (8E8) (CBMAB-0992-YC)
-
Mouse Anti-FOXL1 Recombinant Antibody (CBXF-0845) (CBMAB-F0462-CQ)
-
Rabbit Anti-DLK1 Recombinant Antibody (9D8) (CBMAB-D1061-YC)
-
Mouse Anti-ADGRL2 Recombinant Antibody (V2-58519) (CBMAB-L0166-YJ)
-
Mouse Anti-NSUN6 Recombinant Antibody (D-5) (CBMAB-N3674-WJ)
-
Rabbit Anti-ABL1 (Phosphorylated Y185) Recombinant Antibody (V2-443434) (PTM-CBMAB-0001YC)
-
Mouse Anti-ESR1 Recombinant Antibody (Y31) (CBMAB-1208-YC)
-
Mouse Anti-ALB Recombinant Antibody (V2-55272) (CBMAB-H0819-FY)
-
Mouse Anti-GFAP Recombinant Antibody (5) (CBMAB-G0346-LY)
-
Mouse Anti-CIITA Recombinant Antibody (CBLC160-LY) (CBMAB-C10987-LY)
-
Mouse Anti-ARG1 Recombinant Antibody (CBYCL-103) (CBMAB-L0004-YC)
-
Mouse Anti-GPRC5C Recombinant Antibody (CBFYH-0464) (CBMAB-H0521-FY)
-
Rabbit Anti-ALK (Phosphorylated Y1278) Recombinant Antibody (D59G10) (PTM-CBMAB-0035YC)
-
Mouse Anti-APCS Recombinant Antibody (CBYC-A663) (CBMAB-A3054-YC)
-
Mouse Anti-GST Recombinant Antibody (CBLG1-1938) (CBMAB-G5371-LY)
-
Mouse Anti-AKT1 (Phosphorylated S473) Recombinant Antibody (V2-505430) (PTM-CBMAB-0067LY)
-
Mouse Anti-C5B-9 Recombinant Antibody (CBFYA-0216) (CBMAB-X0304-FY)
-
Mouse Anti-FOSB Recombinant Antibody (CBXF-3593) (CBMAB-F2522-CQ)
-
Mouse Anti-BANF1 Recombinant Antibody (3F10-4G12) (CBMAB-A0707-LY)
For Research Use Only. Not For Clinical Use.
(P): Predicted
* Abbreviations
- AActivation
- AGAgonist
- APApoptosis
- BBlocking
- BABioassay
- BIBioimaging
- CImmunohistochemistry-Frozen Sections
- CIChromatin Immunoprecipitation
- CTCytotoxicity
- CSCostimulation
- DDepletion
- DBDot Blot
- EELISA
- ECELISA(Cap)
- EDELISA(Det)
- ESELISpot
- EMElectron Microscopy
- FFlow Cytometry
- FNFunction Assay
- GSGel Supershift
- IInhibition
- IAEnzyme Immunoassay
- ICImmunocytochemistry
- IDImmunodiffusion
- IEImmunoelectrophoresis
- IFImmunofluorescence
- IGImmunochromatography
- IHImmunohistochemistry
- IMImmunomicroscopy
- IOImmunoassay
- IPImmunoprecipitation
- ISIntracellular Staining for Flow Cytometry
- LALuminex Assay
- LFLateral Flow Immunoassay
- MMicroarray
- MCMass Cytometry/CyTOF
- MDMeDIP
- MSElectrophoretic Mobility Shift Assay
- NNeutralization
- PImmunohistologyp-Paraffin Sections
- PAPeptide Array
- PEPeptide ELISA
- PLProximity Ligation Assay
- RRadioimmunoassay
- SStimulation
- SESandwich ELISA
- SHIn situ hybridization
- TCTissue Culture
- WBWestern Blot
Online Inquiry