ALDH6A1

ALDH6A1 is a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible o
Full Name
Aldehyde Dehydrogenase 6 Family Member A1
Function
Plays a role in valine and pyrimidine metabolism. Binds fatty acyl-CoA.
Biological Process
Branched-chain amino acid catabolic process Source: Reactome
Brown fat cell differentiation Source: Ensembl
Thymine catabolic process Source: BHF-UCL
Thymine metabolic process Source: UniProtKB
Valine catabolic process Source: BHF-UCL
Valine metabolic process Source: UniProtKB
Cellular Location
Mitochondrion
Involvement in disease
Methylmalonate semialdehyde dehydrogenase deficiency (MMSDHD): A metabolic disorder characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.
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Anti-ALDH6A1 antibodies

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Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1, κ
Specificity: Human, Mouse, Rat
Clone: C9
Application*: E, IC, IF, IH, WB
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: 6H9B7
Application*: WB, FC, E, IH, IF
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: CBT4230
Application*: WB, IH, IC, F
Target: ALDH6A1
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: CBT3858
Application*: IH, IC, F
More Infomation
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For Research Use Only. Not For Clinical Use.
(P): Predicted
* Abbreviations
  • AActivation
  • AGAgonist
  • APApoptosis
  • BBlocking
  • BABioassay
  • BIBioimaging
  • CImmunohistochemistry-Frozen Sections
  • CIChromatin Immunoprecipitation
  • CTCytotoxicity
  • CSCostimulation
  • DDepletion
  • DBDot Blot
  • EELISA
  • ECELISA(Cap)
  • EDELISA(Det)
  • ESELISpot
  • EMElectron Microscopy
  • FFlow Cytometry
  • FNFunction Assay
  • GSGel Supershift
  • IInhibition
  • IAEnzyme Immunoassay
  • ICImmunocytochemistry
  • IDImmunodiffusion
  • IEImmunoelectrophoresis
  • IFImmunofluorescence
  • IGImmunochromatography
  • IHImmunohistochemistry
  • IMImmunomicroscopy
  • IOImmunoassay
  • IPImmunoprecipitation
  • ISIntracellular Staining for Flow Cytometry
  • LALuminex Assay
  • LFLateral Flow Immunoassay
  • MMicroarray
  • MCMass Cytometry/CyTOF
  • MDMeDIP
  • MSElectrophoretic Mobility Shift Assay
  • NNeutralization
  • PImmunohistologyp-Paraffin Sections
  • PAPeptide Array
  • PEPeptide ELISA
  • PLProximity Ligation Assay
  • RRadioimmunoassay
  • SStimulation
  • SESandwich ELISA
  • SHIn situ hybridization
  • TCTissue Culture
  • WBWestern Blot
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