Human Recombinant TPM3&ROS1, Active protein, GST Tag (V2LY-0526-LY7333)
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Basic Information
Formulations & Storage [For reference only, actual COA shall prevail!]
Target
Biological Process muscle contraction Source:GO_Central1 Publication
A form of nemaline myopathy with autosomal dominant or recessive inheritance. Nemaline myopathies are disorders characterized by muscle weakness of varying onset and severity, and abnormal thread-like or rod-shaped structures in muscle fibers on histologic examination. Autosomal dominant NEM1 is characterized by a moderate phenotype with onset between birth and early second decade of life. Weakness is diffuse and symmetric with slow progression often with need for a wheelchair in adulthood. The autosomal recessive form has onset at birth with moderate to severe hypotonia and diffuse weakness. In the most severe cases, death can occur before 2 years. Less severe cases have delayed major motor milestones, and these patients may walk, but often need a wheelchair before 10 years.
Myopathy, congenital, with fiber-type disproportion (CFTD):
A genetically heterogeneous disorder in which there is relative hypotrophy of type 1 muscle fibers compared to type 2 fibers on skeletal muscle biopsy. However, these findings are not specific and can be found in many different myopathic and neuropathic conditions.
Cap myopathy 1 (CAPM1):
A rare congenital skeletal muscle disorder characterized by the presence of cap-like structures which are well demarcated and peripherally located under the sarcolemma and show abnormal accumulation of sarcomeric proteins. Clinical features are early onset of hypotonia and slowly progressive muscle weakness. Respiratory problems are common.
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Please try the standard protocols which include: protocols, troubleshooting and guide.
Enzyme-linked Immunosorbent Assay (ELISA)
Flow Cytometry
Immunofluorescence (IF)
Immunohistochemistry (IHC)
Immunoprecipitation (IP)
Western Blot (WB)
Enzyme Linked Immunospot (ELISpot)
Proteogenomic
Other Protocols
Alternative Versions
Human Recombinant TPM3 protein, His Tag (CAT#: V2LY-0526-LY7330)
Human Recombinant TPM3&PDGFRB, Active protein, GST Tag (CAT#: V2LY-0526-LY7332)
Human Recombinant TPM3&TRKA, Active protein, GST Tag (CAT#: V2LY-0526-LY7334)
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Human Recombinant TPM3-ALK, Active protein, GST Tag (CAT#: V2LY-0526-LY7331)
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Human Recombinant TPM3&TRKA, Active protein, GST Tag (CAT#: V2LY-0526-LY7334)
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Human Recombinant TPM3&PDGFRB, Active protein, GST Tag (CAT#: V2LY-0526-LY7332)
Human Recombinant TPM3 protein, His Tag (CAT#: V2LY-0526-LY7330)
Custom Antibody Labeling
We also offer labeled antibodies developed using our catalog antibody products and nonfluorescent conjugates (HRP, AP, Biotin, etc.) or fluorescent conjugates (Alexa Fluor, FITC, TRITC, Rhodamine, Texas Red, R-PE, APC, Qdot Probes, Pacific Dyes, etc.).
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