SI
This gene encodes a sucrase-isomaltase enzyme that is expressed in the intestinal brush border. The encoded protein is synthesized as a precursor protein that is cleaved by pancreatic proteases into two enzymatic subunits sucrase and isomaltase. These two subunits heterodimerize to form the sucrose-isomaltase complex. This complex is essential for the digestion of dietary carbohydrates including starch, sucrose and isomaltose. Mutations in this gene are the cause of congenital sucrase-isomaltase deficiency.
Full Name
sucrase-isomaltase (alpha-glucosidase)
Function
Plays an important role in the final stage of carbohydrate digestion. Isomaltase activity is specific for both alpha-1,4- and alpha-1,6-oligosaccharides.
Biological Process
Biological Process polysaccharide digestionTAS:Reactome
Biological Process sucrose catabolic processManual Assertion Based On ExperimentIDA:UniProtKB
Biological Process sucrose catabolic processManual Assertion Based On ExperimentIDA:UniProtKB
Cellular Location
Apical cell membrane
Topology
Cytoplasmic: 2-12
Helical: 13-32
Lumenal: 33-1827
Helical: 13-32
Lumenal: 33-1827
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Anti-SI antibodies
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Target: SI
Host: Mouse
Antibody Isotype: IgG1
Specificity: Human
Clone: HBB2/614/88
Application*: E, P, IF, IH, IP, WB
Target: SI
Host: Mouse
Antibody Isotype: IgG2b
Specificity: Human
Clone: HBB2/219/20
Application*: E, IF, IH, IP
Target: SI
Host: Mouse
Antibody Isotype: IgG2b, κ
Specificity: Human
Clone: 1A8
Application*: WB, E
Target: SI
Host: Mouse
Antibody Isotype: IgG2b, κ
Specificity: Human
Clone: CBXS-3838
Application*: E, WB
Target: SI
Host: Mouse
Specificity: Human
Clone: CBXS-5675
Application*: IP
Target: SI
Host: Mouse
Specificity: Human
Clone: CBXO-0055
Application*: WB, IC, P, C, E
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For Research Use Only. Not For Clinical Use.
(P): Predicted
* Abbreviations
- AActivation
- AGAgonist
- APApoptosis
- BBlocking
- BABioassay
- BIBioimaging
- CImmunohistochemistry-Frozen Sections
- CIChromatin Immunoprecipitation
- CTCytotoxicity
- CSCostimulation
- DDepletion
- DBDot Blot
- EELISA
- ECELISA(Cap)
- EDELISA(Det)
- ESELISpot
- EMElectron Microscopy
- FFlow Cytometry
- FNFunction Assay
- GSGel Supershift
- IInhibition
- IAEnzyme Immunoassay
- ICImmunocytochemistry
- IDImmunodiffusion
- IEImmunoelectrophoresis
- IFImmunofluorescence
- IGImmunochromatography
- IHImmunohistochemistry
- IMImmunomicroscopy
- IOImmunoassay
- IPImmunoprecipitation
- ISIntracellular Staining for Flow Cytometry
- LALuminex Assay
- LFLateral Flow Immunoassay
- MMicroarray
- MCMass Cytometry/CyTOF
- MDMeDIP
- MSElectrophoretic Mobility Shift Assay
- NNeutralization
- PImmunohistologyp-Paraffin Sections
- PAPeptide Array
- PEPeptide ELISA
- PLProximity Ligation Assay
- RRadioimmunoassay
- SStimulation
- SESandwich ELISA
- SHIn situ hybridization
- TCTissue Culture
- WBWestern Blot
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